A review of the research literature related to Williams 'elfin facies' Syndrome (a condition including mental retardation and cardiac anomalies), a case study, and the results of an early intervention program, are reported. The medical aspects of the syndrome have been reported with sufficient consistency for a profile to emerge. Psychological variables have been reported with less frequency and educational programing needs have received little attention. Etiology and prognosis have been considered indeterminate. The case study reported a 27 month intervention program (9 months to 36 months) and included an abbreviated history, comparison of case to syndrome profile and the results of educational programing. Recommendations for appropriate educational programing are made in light of previous research and results of the reported case. (Author)