ERIC Number: EJ927749
Record Type: Journal
Publication Date: 2011-Feb
Abstractor: As Provided
Reference Count: 46
The Prevalence and Phenomenology of Self-Injurious and Aggressive Behaviour in Genetic Syndromes
Arron, K.; Oliver, C.; Moss, J.; Berg, K.; Burbidge, C.
Journal of Intellectual Disability Research, v55 n2 p109-120 Feb 2011
Background: Self-injurious and aggressive behaviours are reported as components of some behavioural phenotypes but there are few studies comparing across syndrome groups. In this study we examined the prevalence of these behaviours and the associated person characteristics in seven genetic syndromes. Methods: Questionnaire data on self-injury and aggression, mood, hyperactivity, autism spectrum disorder and repetitive behaviour were collected on Angelman (AS, n = 104), Cornelia de Lange (CdLS, 101), Cri du Chat (CdCS, 58), Fragile X (FXS, 191), Lowe (LS, 56), Prader-Willi (PWS, 189) and Smith-Magenis (SMS, 42) syndromes. Results: A significantly higher prevalence of self-injury was evident in CdCS, CdLS, FXS, PWS, LS and SMS. The prevalence of aggression was significantly heightened in AS and SMS. Self-injury was associated with repetitive and impulsive behaviour in CdLS, FXS, PWS and LS. Impulsivity and overactivity were significantly higher in those showing aggression across all syndrome groups. Conclusions: These data quantify the risk for self-injury and aggression in the syndromes studied with implications for early intervention. The associations between these behaviours and person characteristics both within and between syndromes warrant further research.
Descriptors: At Risk Persons, Intervention, Incidence, Injuries, Hyperactivity, Genetics, Phenomenology, Self Destructive Behavior, Genetic Disorders, Behavior Problems, Questionnaires, Emotional Response, Pervasive Developmental Disorders, Comparative Analysis
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Publication Type: Journal Articles; Reports - Research
Education Level: N/A
Authoring Institution: N/A