ERIC Number: EJ927746
Record Type: Journal
Publication Date: 2011-Feb
Abstractor: As Provided
Reference Count: 92
Prevalence, Phenomenology, Aetiology and Predictors of Challenging Behaviour in Smith-Magenis Syndrome
Sloneem, J.; Oliver, C.; Udwin, O.; Woodcock, K. A.
Journal of Intellectual Disability Research, v55 n2 p138-151 Feb 2011
Background: The prevalence, phenomenology aetiology and correlates of four forms of challenging behaviour in 32 children and adults with Smith-Magenis syndrome (SMS) were investigated. Methods: Cognitive assessments, questionnaires and semi-structured interviews were used to gather data on intellectual disability, verbal and physical aggression, destructive behaviour and self-injury and on characteristics known to be associated with aggression. Results: Aggression in SMS was more prevalent (87%), but not more severe than aggression in contrast groups. Aggressive behaviour was more frequently associated with environmental contingencies (e.g. attention, escape and access to tangibles) than self-injury and destructive behaviours. Severity of challenging behaviours was associated with high impulsivity. Conclusion: Aggression is seen in the majority of people with SMS. Results suggest that behavioural disinhibition and operant social reinforcement are associated with the manifestation of aggression.
Descriptors: Aggression, Incidence, Mental Retardation, Injuries, Interviews, Social Reinforcement, Phenomenology, Etiology, Children, Adults, Genetic Disorders, Evaluation, Questionnaires, Self Destructive Behavior, Predictor Variables
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Publication Type: Journal Articles; Reports - Research
Education Level: N/A
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